First Description of Bilateral Lung Transplantation in Patient with Birt–Hogg–Dubé Syndrome: A Case Report and Surgical Feasibility Insight
Tomasz Stącel, Jakub Pawlak, Agnieszka Olma, Mirosław Nęcki, Anna Pióro-Lewandowska, Małgorzata Węcławek, Igor Gumennyi, Piotr Pasek, Witold Bratkowski, Mariusz Śledź, Piotr Przybyłowski, Tomasz Hrapkowicz, Maciej Urlik, Payaningal R Somanath · 2025
Read First Description of Bilateral Lung Transplantation in Patient with Birt–Hogg–Dubé Syndrome: A Case Report and Surgical Feasibility Insight by Tomasz Stącel, Jakub Pawlak, Agnieszka Olma, Mirosław Nęcki, Anna Pióro-Lewandowska, Małgorzata Węcławek, Igor Gumennyi, Piotr Pasek, Witold Bratkowski, Mariusz Śledź, Piotr Przybyłowski, Tomasz Hrapkowicz, Maciej Urlik, Payaningal R Somanath (2025) in the Tower of Babel, a free online library of public-domain works preserved in clean, searchable text. No sign-up. The full text is served as a plain-text file at a predictable URL, where text is present: https://antarctic-labs.com/tower-of-babel/pmc-12734903.txt.
Description
Birt–Hogg–Dubé Syndrome (BHDS) is a rare autosomal dominant disorder associated with mutations in the Foliculin gene (FLCN), characterized by skin lesions, renal tumors (often malignant or leading to malignancy), and lung cysts, often leading to spontaneous pneumothorax. Lung function is generally preserved in these patients, which is why lung transplantation (LTx) has not been performed in this population to date.
Catalog record
| CREATOR | Tomasz Stącel, Jakub Pawlak, Agnieszka Olma, Mirosław Nęcki, Anna Pióro-Lewandowska, Małgorzata Węcławek, Igor Gumennyi, Piotr Pasek, Witold Bratkowski, Mariusz Śledź, Piotr Przybyłowski, Tomasz Hrapkowicz, Maciej Urlik, Payaningal R Somanath |
|---|---|
| YEAR | 2025 |
| COLLECTION | PAPERS |
| FORMAT | TXT |
| FILE SIZE | 24 KB |
| VERSION | 1.0 |
| LICENSE | CC BY 4.0 |
| RIGHTS | CC BY |
| SOURCE | Europe PMC |